TY -的A2许Tsai-Ching盟——Farshad Sohail AU -菲格罗亚罗德里格斯,费尔南多AU - Halalau,亚历山德拉盟外长,约瑟夫盟,拉斯穆森科里盟——Pevzner马丁PY - 2019 DA - 2019/09/29 TI -中枢神经系统的影响和共同变量的模仿免疫缺陷(CVID):病例报告和文献回顾SP - 7623643六世- 2019 AB -有一个缺乏信息的共同变量的影响中枢神经系统免疫缺陷(CVID)。30岁的女人反复上呼吸道感染史,白癜风,免疫血小板减少性紫癜出现右侧肢体麻木。磁共振成像(MRI) hyperintensity胸椎的显示信号。核磁共振成像的大脑展示天赋hyperintensity正确的额中回。脑脊髓液是不起眼的。血清免疫球蛋白显示低丙球蛋白血症。支气管和随后的纵隔活组织检查均为阴性结节病和恶性肿瘤。没有发现传染性病因。她用糖皮质激素治疗,静脉注射免疫球蛋白(丙种球蛋白)替代疗法CVID-associated脊髓炎。随访MRI显示改善; however, her numbness persisted despite these treatments, which led to an outside physician adding methotrexate for their suspicion of sarcoidosis. Her symptoms remained stable for two years, but when the methotrexate dose was weaned, her numbness worsened. Upon review, the treatment team refuted the diagnosis of sarcoidosis but continued treatment with prednisone, IVIG, and methotrexate for CVID-associated myelitis, from which her symptoms have stabilized. Here, we discuss CVID-associated neurological complications, its similarities to sarcoidosis, and a literature review with treatment regimens and outcomes. SN - 2090-6889 UR - https://doi.org/10.1155/2019/7623643 DO - 10.1155/2019/7623643 JF - Case Reports in Rheumatology PB - Hindawi KW - ER -