TY - JOUR A2 - Hayashi, Takaaki AU - Stahnke, Thomas AU - Erbersdobler, Andreas AU - Knappe, Steffi AU - Guthoff, Rudolf F. AU - Kilangalanga, Ngoy J. PY - 2018 DA - 2018/10/09 TI -治疗先天性临床眼球缺损合并眼眶囊肿:SP - 5010915 VL - 2018 AB -早期发育性视囊泡缺乏可导致先天性无眼症，定义为眼睛完全缺失，可与先天性小眼症区分，后者存在眼球雏形。本文报告一例罕见的小儿先天性无眼并左眼眶囊肿。患者为一名无其他先天性缺陷的14个月女童，在刚果民主共和国金沙萨圣约瑟夫医院接受了手术和假体治疗。手术是在全身麻醉下进行的。囊肿被穿刺，囊肿壁被完全切除。在眶尖附近发现了一些色素元素，包括虹膜、睫状体、脉络膜或视网膜残余。标本用福尔马林溶液固定，进行组织学检查。进行了囊肿切除手术，包括眼窝加深术。术后伤口愈合顺利，所有随访检查均获得满意的美容结果。 Histological examination revealed rudimentary ocular structures similar to degenerated lens tissue with a typical, PAS-positive capsule. Additionally, pigmented epithelial structures, which seem to be of ciliary body, iris, and choroidal or retinal-type epithelium origin, could be detected, prompting the final diagnosis, microphthalmia with dominant cyst formation. SN - 2090-6722 UR - https://doi.org/10.1155/2018/5010915 DO - 10.1155/2018/5010915 JF - Case Reports in Ophthalmological Medicine PB - Hindawi KW - ER -